A case of unusual longevity of tetralogy of Fallot confirmed by cardiac catheterization
Kanji Iga, Kenjiro Hori, Tadashi Matsumura, Hiromitsu Gen, Shouji Kitaguchi, Go Tomonaga and Toshitake Tamamura
Summary
We describe a 61-year-old woman with tetralogy of Fallot and dextrocardia
with complete situs inversus. The functional status of this patient was
New York Heart Association (NYHA) class II and the systemic blood pressure
was 100/54mmHg. The hematocrit was 54.4 % and the arterial partial pressure
of oxygen was 53 mmHg. On cardiac catheterization, both pulmonary valvular
and infundibular stenoses were of equal severity and the aorta and main
pulmonary artery were of equal size. We think that this patient has survived
to this unusual age for tetralogy of Fallot because of unusually low systemic
pressure and a proper balance between the ventricular septal defect and
the pulmonary stenosis.